Site Loader

Hemifacial hypertrophy abbreviated as (HFH) is rare congenital disease characterized by unilateral enlargement of the head and teeth. It is classified as true. Depending on involvement of soft tissues, teeth, and bones, he further classified hemifacial hypertrophy into (a) true hemifacial hypertrophy and. Two cases of congenital hemifacial hypertrophy are described. To our knowledge , this is the first report of this syndrome in a black African population. Possible.

Author: Kagalkis Daikinos
Country: Hungary
Language: English (Spanish)
Genre: Music
Published (Last): 28 August 2005
Pages: 305
PDF File Size: 2.96 Mb
ePub File Size: 9.38 Mb
ISBN: 209-5-21690-674-9
Downloads: 41496
Price: Free* [*Free Regsitration Required]
Uploader: Daijin

Intraoral photograph showing enlargement of right side of the yemifacial with enlarged papillae. The right submental region, submandibular region, parapharyngeal space, pterygopalatine fossa, soft palate, tongue, and floor of mouth were involved Figure Report of two cases. Hyprrtrophy pattern on right side is far advanced than the left side with broad and thick alveolar process.

Report of five new cases and review of literature. Widening of the palate and enlargement of the alveolar bone of the affected side were noted in the present case as described in the literature [ 4 ]. The teeth, heifacial, and maxilla should be carefully scrutinized for deformities to help one reach the correct diagnosis. In this theory, Pollock and colleagues stated that neural fold appears to be larger on one side compared to the other part of structure.

Orofacial soft tissues — Soft tissues around the mouth.

According to Noe and Bergman, mitochondrial damage overripened one-half of the fertilized egg resulting in excess generation of cells [ 9 ]. The mass of the ipsilateral parotid gland and that of the muscles of mastication were increased in our patient as reported by many authors hypertropny 413 ]. Enlargement and deformity of all tissue of the face, including teeth and their related tissues in the jaw, are the key findings in the diagnosis of hemifacial hypertrophy 5.


Large volume liposuction may require higher laser energies, increasing the risk of burns and skin necrosis. Mouth opening and the range of movement was adequate. According to Yoshimoto et al. The purpose of this report is to present the case of a child with congenital hemifacial hyperplasia and to supplement existing clinical knowledge.

Case Reports in Dentistry

Involvement of orofacial structures is related to asymmetric morphogenesis of teeth, bone, and soft tissues. A report on complications.

However, the patients frequently required blood transfusions due to blood loss. A thirty-nine-year-old male patient reported to the Department of Oral Medicine and Radiology with a chief complaint of asymptomatic swelling in his right cheek region since birth.

J Cutan Aesthet Surg. Depending on involvement of soft tissues, teeth, and bones, he further classified hemifacial hypertrophy into a true hemifacial hypertro;hy and b partial hemifacial hypertrophy.

Congenital partial hemihypertrophy involving marked malocclusion. There was an obvious enlargement of tongue on the right side, which began abruptly at the midline [ Figure 2 ]. An excisional biopsy of the growth at the left buccal mucosa was found to be lipomatous in origin.

The patient refused to undergo extensive surgical procedures as hypertdophy lesion was asymptomatic.

Congenital hemifacial hyperplasia

Sometimes HFH may resemble cystic hygroma, especially if the lymphatic anomaly is located inferior to the jaws and in the neck region. Check for errors and try again. Introduction Congenital Hemifacial Hyperplasia CHH is a yhpertrophy developmental malformation exhibited by a unilateral enlargement of hard and soft tissues of the face.

Khanna and Andrade[ 2 ] performed extensive surgeries in three stages using a hard and soft tissue debulking to achieve an acceptable result, while Pollock used osteotomies and recontouring to correct the bony deformities. Table of Contents Alerts.


Congenital hemifacial hyperplasia

Burchfield and Escobar described a family in which several members showed mandibular asymmetry and maxillary hypoplasia. Various theories have been proposed. American Journal of Medical Genetics.

Abstract Congenital hemihyperplasia is a rare developmental disorder characterized by unilateral overgrowth of one or more body parts resulting in marked asymmetry. Multisystem involvement has resulted in etiological heterogeneity including heredity, chromosomal abnormalities, atypical forms of twinning, altered intrauterine environment, and endocrine dysfunctions; however, no single theory explains the etiology adequately.

No other physical abnormality was noted. Dentition abnormalities are with respect to crown size, root size, and shape and rate of development. In the deciduous dentition, the second molar and in the permanent dentition the cuspids were the most hupertrophy affected teeth followed by the first molars and premolars.

Soft tissue enlargement was seen on the right side of the face and also encircling the symphysis. Orofacial soft tissues — Soft tissues hemifavial the mouth Actinomycosis Angioedema Basal hypeetrophy carcinoma Cutaneous sinus of dental origin Cystic hygroma Gnathophyma Ludwig’s angina Macrostomia Melkersson—Rosenthal syndrome Microstomia Noma Hemifavial Crohn’s disease Orofacial granulomatosis Perioral dermatitis Pyostomatitis vegetans.

Br J Oral Maxillofac Surg. Report of four cases. Radiographically, this lesion presents with hard tissue and soft tissue enlargement on the affected side. Asymmetry is one of the more unusual and interesting errors of human reproduction. Enlarged right maxillary and mandibular alveolar arches, upper and lower labial mucosa, and buccal mucosa were observed.